Page 49 - Journal of Structural Heart Disease Volume 5, Issue 4

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Meeting Abstracts
However, the stents showed some degree of recoil (mean recoil 10.4%, range 0 – 21%).
Conclusions: The use of DES for branch pulmonary artery stenosis in small vessels is a safe alternative with potential for further expansion and fracture to achiever larger diam- eters. DES showed no in-stent restenosis at a mean fol- low-up of 3 months, however, some degree of stent recoil was common. Longer follow-up is needed to better assess restenosis rates and vessel growth.
62. TRANSCATHETER INTERVENTION IN A PRE-TERM CHILD WITH SCIMITAR SYNDROME.
Iñaki Navarro Castellanos1,2, Alberto Zárate Fuentes1,
Pedro Ivan Barrera Martínez2, Leslie Solano Ibarra2, Manuel Soriano2
1h.R.L.A.L.M Issste, Mexico City, Mexico. 2hip, Mexico City, Mexico
Background: Scimitar syndrome is a rare congenital heart disease. Surgical correction remains the gold-stan- dard therapy. However, the non-surgical intervention has been reported as effective in selected cases with scimitar syndrome.
Pulmonary sequestration is a condition in which a seg- ment or lobe of dysplastic lung tissue exists with no com- munication with the rest of the tracheobronchial tree and receives an anomalous systemic vascular supply, separated from the rest of the lung.
Arterial supply is from systemic vessels–most commonly descending thoracic aorta (73%), and the remaining 27% from these other arteries: the cranial portion of the abdom- inal aorta, celiac trunk, splenic artery, as well as intercostal arteries.
Case presentation: We report on a 15 days-old boy, of 1.6 Kg with scimitar syndrome who underwent stepwise transcatheter intervention as an alternative treatment. Embolization of the aortopulmonary collateral and occlu- sion of the Patent Ductus Arteriosus were performed using Amplatzer PDA AS, in both defects, without arterial access. First the aortopulmonary collateral crossing the PDA and finally de PDA.
The patient post-catheterization course was uneventful. The right cardiac chamber and pulmonary arterial pressure returned to normal during follow up.
Conclusions: This report highlights the role of minimal invasive approach in the management of Scimitar syn- drome in pediatric patients to diminish the morbidity and
mortality associated with more invasive procedures or late management.
63. A SINGLE CENTER REVIEW OF DIAGNOSTIC AND THERAPEUTIC STRATEGIES OF PATIENTS WITH UNILATERAL PULMONARY ARTERY AGENESIS
Ah Young Kim, Han Ki Park, Jae Young Choi
Yonsei university health system, Seoul, Korea, Republic of
Unilateral pulmonary artery agenesis (UPAA) is a rare con- genital anomaly due to a malformation of the sixth aor- tic arch of the affected side during embryogenesis. It can present as an isolated lesion or with other congenital heart diseases. The diagnosis is usually set at adolescence while being asymptomatic, however with the development of various imaging modalities, the importance of early diag- nosis and revascularization is emerging.
This retrospective review study included cases of UPAA in the single tertiary center from March. 2005 through March. 2019. Of the 15 patients identified, 13 had isolated UPAA (5 with Patent ductus arteriosus).
Median age of diagnosis was 5.3 (0.0 – 43.0) years old and 4 were asymptomatic at that time but incidentally found by chest x-ray. Symptoms including dyspnea, desaturation, chronic cough, frequent pulmonary infections and hemop- tysis were found in majority of patients (12/15) during follow up periods. Patients who have delayed diagnosis were not encouraged or feasible because the intrapulmo- nary arteries had been found to be severely narrowed or completely obstructed. 5 (33%) patients were undertaken staged repair to promote distal PA growth and lung devel- opment. The first stage was PDA stenting, followed by surgical anastomosis in the second stage. They all stable during mid-term follow-up (7.1 ± 5.3 years) and results in remarkable growth of the affected pulmonary artery from -4.7 ± 2.5 of z-score at 1st palliation to -1.5 ± 1.2 at last fol- low up point. There was 1 case of mortality who was suf- fered from tracheal stenosis which is known as associated with unilateral lung hypoplasia.
Although there is no consensus on treatment of UPAA, it is getting important to establish an early diagnosis and pro- vide adequate treatment for this disease. Careful aware- ness of diagnosis and early search for the occult PA will help.
64. USE CHEATHAM PLATINUM STENT TO RESOLVE SUPRAVALVAR PULMONARY STENOSIS IN A 13-YEAR- OLD BOY LATE AFTER ARTERIAL SWITCH OPERATION FOR TRANSPOSITION OF GREAT ARTERY
Hijazi, Z
22nd Annual PICS/AICS Meeting