Page 51 - Journal of Structural Heart Disease Volume 2, Issue 6

Meeting Abstracts
278
Figure 1 (#0090).
#0089
TRANSCATHETER THERAPY OF RAGHIB SYNDROME (RIGHT SUPERIOR VENA CAVA DRAINAGE INTO
THE LEFT ATRIUM) UTILIZING A 3D PRINTED MODEL Daisuke Kobayashi, Daniel Turner, Thomas Forbes
Children’s Hospital of Michigan, Detroir, MI, USA
Introduction: Raghib syndrome is a rare congenital anomaly charac- terized by right superior vena cava (SVC) drainage into the left atrium and causes cyanosis and infection. Surgical correction is the choice of therapy and transcatheter treatment has not been described. We report a case of successful transcatheter treatment of Raghib syn- drome utilizing a 3D printed model.
Case: A 32 year old male (104 kg) with history of brain abscess was referred for anomalous drainage of right SVC into the left atrium. There was left SVC draining into the right atrium through the coronary sinus, without a bridging vein. His baseline saturation was 90%. Cardiac mag- netic resonance imaging delineated that right upper pulmonary vein drained into the right SVC. We aimed to occlude the proximal right SVC with device, achieving normal drainage of right upper pulmonary vein into the left atrium and exclusion of a right-to-left shunting, diversion of systemic venous ow from right SVC into inferior vena cava system through the azygos vein. The pre-procedural planning was augmented by the 3D Printed model. He underwent successful occlusion of proxi- mal Right SVC with a 16 mm Amplatzer muscular VSD occluder. There was no signi cant increase of right SVC pressures post-device. At 6 month follow up, his saturation improved to 97%
Conclusion: Transcatheter therapy of Raghib syndrome was success- ful. Pre-procedural planning was critical, augmented by a 3D printed model in this case.
#0090
INSTITUTIONAL VARIATION OF SIGNIFICANT ADVERSE EVENT RATE IN THE PEDIATRIC CATHETERIZATION LABORATORIES – CONGENITAL CARDIAC INTERVENTION STUDY CONSORTIUM (CCISC) RISK REGISTRY STUDY
Daisuke Kobayashi1, Thomas Forbes1, David Nykanen2
1Children’s Hospital of Michigan, Detroit, MI, USA 2Arnold Palmer Hospital For Children, Orlando, FL, USA
Background: Comparison of signi cant adverse event (SAE) between institutions is not straightforward because the risk associated with catheterization varies based on procedural complexity and heteroge- neous patient characteristics. CCISC investigators recently proposed CRISP (Catheterization RISk Score for Pediatrics) to predict the risk of adverse events for children undergoing catheterization.
Objective: The study aim is to utilize CRISP Category for description of practice variation and comparison of SAE rate between institutions accounting for case volume.
Method: This was a retrospective study of CCISC Risk Registry. SAE rate was assessed by the funnel plots accounting for case volume in each CRISP Category. Funnel plots were depicted with 95% and 97% upper control limit of the overall mean SAE rate accounting for case volume.
Results: A total of 3711 pediatric patients were enrolled from 15 par- ticipating sites in 2015. SAE rates were 1.8% (13/709, Category 1), 2.0% (30/1464, Category 2), 5.3% (58/1086, Category 3), 12.0% (45/376, Category 4) and 24.2% (8/33, Category 5) [p<0.001]. The funnel plots were created for each CRISP category (Figure).
Conclusion: Funnel plots of SAE rate in CRIPS categories were useful to show the institutional performance in a clearly visible fashion.
#0091
TRANSCATHETER CLOSURE OF VENTRICULAR SEPTAL DEFECTS: ECHOCARDIOGRAPHY BEFORE, DURING AND AFTER PROCEDURE
M. Fernanda Biancolini, Julio C. Biancolini, Ana De Dios, Jesus Damsky Barbosa
Elizalde Children’s Hospital, Buenos Aires, Argentina
Introduction: The purpose of this study is to analyze the utility of echocardiography in transcatheter VSD closure.
Journal of Structural Heart Disease, December 2016
Volume 2, Issue 6:241-306