Page 29 - Journal of Structural Heart Disease Volume 4, Issue 1

Case Report
20
Despite good immediate results in our case, a fu- ture increase in systolic pressure gradient is possible due to growth of the child and neointimal prolifer- ation [15, 16]. This complication often occurs after stenting of vessels, especially in children with Williams syndrome or other genetic defects accompanied by connective tissue dysplasia, which are characterized by a tendency to increased proliferation of the endo- thelium [17]. However, in our case of hybrid manage- ment of an urgent obstruction of the ascending aorta and aortic arch, we used Valeo stents, which have the capacity for further expansion to an adult size if and when needed [18]. Therefore, our case demonstrates
the possibility of intraoperative diagnosis and elim- ination of a formidable complication such as acute aortic dissection using endovascular technologies in pediatric cardiac surgery.
Con ict of Interest
The authors have no con ict of interest relevant to this publication.
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Journal of Structural Heart Disease, February 2018
Volume 4, Issue 1:17-20
Cite this article as: Pursanov MG, Sha- talov KV, Sobolev AV, Arnautova IV. The First Case of Successful Stenting of the Dissection of the Ascending Aorta and the Aortic Arch that Occurred During Surgical Correction of the Supralvular Aortic Stenosis in a Child with the Wil- liams Syndrome. Structural Heart Dis- ease. 2018;4(1):17-20. DOI: https://doi. org/10.12945/j.jshd.2018.031.17