Page 140 - Journal of Structural Heart Disease Volume 5, Issue 4

Meeting Abstracts
202
Univentricular
Hybrid/PAB/ Damus
Post Glenn
Post Fontan
Hypoplastic Left Heart Syndrome
DILV
Univentricular miscellaneous
N=2,
(2.5 and 2.9kg)
N=1, (4.35kg)
No previous Interventions
N=1, (2.1kg)
N=5, (Median wt 10.6)
N=1, (9.8 kg)
Post Surgery for palliation
N=6 (Median wt 5.375kg)
N=1 (16.7 kg) N=1,(15.8kg)
We included all non-confluent branch pulmonary arter- ies with or without alternate lung supply and excluded acquired disconnection of pulmonary arteries.
Results: We identified 50 patients with CDPA. 85% of our population presented during infancy (age range from 4 days to 17years). The majority of CDPA were associated with Cono-truncal abnormalities (Tetralogy Of Fallot 13, Truncus arteriosus 9, PA/VSD/MAPCAs 9, Absent Pumonary Valve syndrome 2 and Interrupted Aortic arch 1). 5 cases were heterotaxy syndromes with 2 RAI and 3 LAI. 5 chil- dren had isolated CDPA with normal heart and 6 were in the miscellaneous group. The supply to the disconnected segments was from ductus arteriosus in 22 patients. Median age of patients at first intervention was 10 months (1 to 254 months). Commonest confirmatory diagnostic modality was cardiac catheterization in 35 patients with pulmonary vein wedge injections to confirm presence of disconnected pulmonary artery. 12 patients had interven- tion with stent to maintain patency of the disconnected pulmonary artery with 8 of them requiring recanalisation of the occluded ductal tissue prior to stenting. Mean num- ber of procedures post initial treatment was 5.1 (range 1-9) in our series. One patient had unsuccessful recruitment. Status at last review was satisfactory in 45 patients doing well clinically, 1 with pulmonary hypertension, 1 remains cyanotic. 8 patients had associated genetic syndrome. Mortality in this series was three patients (6%).
Conclusion: Our experience suggests recruitment of CDPA is feasible and safe procedure with good outcomes. Most patients are likely to need initial palliation with cardiac catheterization and intervention before recruitment and full repair. The disconnected pulmonary artery is likely to need multiple interventions.
186. CARDIAC EROSIONS AFTER TRANSCATHETER ATRIAL SEPTAL DEFECT CLOSURE WITH THE OCCLUTECH FIGULLA FLEX DEVICE
Alain Fraisse1, Johanne Auriau2, Helene Bouvaist2, Lars Aaberge3, Tadaaki Abe4, Ingo Dahnert5, Joseph Panzer6, Giuseppe Santoro7, Markus Khalil8, Ziyad M. Hijazi9
1Royal Brompton Hospital, London, United Kingdom. 2University Grenoble Alpes, Grenoble, France. 3Oslo University, Oslo, Norway. 4Nigata City General Hospital, Niigata City, Japan. 5Leipzig Heart Center, Leipzig, Germany. 6Ghent University, Ghent, Belgium. 7University Naples, Massa, Italy. 8University Giessen, Geissen, Germany. 9Sidra Medicine, Doha, Qatar
Background and Method: Cardiac erosion after tran- scatheter closure of secundum atrial septal defect is a rare complication that is mainly reported with the Amplatzer
There were 18 patients who had successful implantation, with 1 procedure related death in a baby who had 2 failed attempts. 1 another patient died during the study period unrelated to the procedure. All stents were patent on last follow up or till the next surgical palliation. There was no re-intervention for dilation of the stent.
Conclusion: Atrial septal stenting is reliable to provide patent atrial communication. It can achieve good hae- modynamic result in restrictive atrial communication at all stages of univentricular palliation.
185. REHABILITATION OF CONGENITALLY DISCONNECTED OR NON-CONFLUENT PULMONARY ARTERIES - ROLE OF DIAGNOSTIC AND INTERVENTIONAL CARDIAC CATHETERISATION Chetan Mehta, Sarvanan Durairaj, John Stickley, David Barron, Oliver Stumper
Birmingham Womens and Childrens Hospital, Birmingham, United Kingdom
Background: Congenital disconnected or non-confluent pulmonary artery (CDPA) is a rare condition which can be associated with other congenital heart disease. With cur- rent technological advances in cross sectional imaging of CT/MRI scan, the role of cardiac catheter is limited. We looked at the role of Cardiac Catheter in diagnosis and rehabilitation of CDPA.
Aim: To identify the role of diagnostic/interventional cardiac catheterization in rehabilitation of congenitally disconnected non-confluent branch pulmonary artery (CDPA). We studied the pattern of presentation, diagnostic modalities and outcomes including death.
Methods: Retrospective review of all children with CDPA between 1989 and 2017 at a single centre. The data was collected from our local database and clinical notes review.
Journal of Structural Heart Disease, August 2019
Volume 5, Issue 4:75-205