Original Research Articles

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Journal of Structural Heart Disease, October 2016, Volume 2, Issue 5:208-212
DOI: 10.12945/j.jshd.2016.013.15

Partial Anomalous Pulmonary Venous ­Return into the Inferior Vena Cava in a 28-Year-Old ­Female: A Variant of Scimitar Syndrome ­Amenable to Interventional Treatment

Scimitar Syndrome Variant

Jana-K. Dieks, MD*, Michael Steinmetz, MD, Thomas Paul, MD, Heike E. Schneider, MD

Department of Pediatric Cardiology and Intensive Care Medicine, University Hospital, Georg-August-University Göttingen, Germany

Abstract

Scimitar syndrome is a rare congenital heart defect ­associated with right-sided partial anomalous pulmonary venous return (PAPVR) into the inferior vena cava (IVC). We describe the case of a 28-year-old female ­diagnosed with PAPVR with a typical curvilinear pattern of the right lower pulmonary vein—the so-called “scimitar sign”—on chest x-ray. Anatomical abnormalities on magnetic resonance imaging included a lower right pulmonary vein draining into the IVC and an ­additional vein connecting all right-sided pulmonary veins toward the left atrium. Because her anatomy was suitable, the patient underwent cardiac catheterization with occlusion of the anomalous right lower ­pulmonary vein with an Amplatzer Vascular Plug with excellent postinterventional results.

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Cite this article as: Dieks J-K, Steinmetz M, Paul T, Schneider HE. Partial Anomalous Pulmonary Venous ­Return into the Inferior Vena Cava in a 28-Year-Old ­Female: A Variant of Scimitar Syndrome ­Amenable to Interventional Treatment – Scimitar Syndrome Variant. Structural Heart Disease 2016;2(5):208-212. DOI: 10.12945/j.jshd.2016.013.15

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