Original Research Articles
Journal of Structural Heart Disease, October 2016, Volume 2, Issue 5:208-212
Partial Anomalous Pulmonary Venous Return into the Inferior Vena Cava in a 28-Year-Old Female: A Variant of Scimitar Syndrome Amenable to Interventional Treatment
Scimitar Syndrome Variant
Department of Pediatric Cardiology and Intensive Care Medicine, University Hospital, Georg-August-University Göttingen, Germany
Scimitar syndrome is a rare congenital heart defect associated with right-sided partial anomalous pulmonary venous return (PAPVR) into the inferior vena cava (IVC). We describe the case of a 28-year-old female diagnosed with PAPVR with a typical curvilinear pattern of the right lower pulmonary vein—the so-called “scimitar sign”—on chest x-ray. Anatomical abnormalities on magnetic resonance imaging included a lower right pulmonary vein draining into the IVC and an additional vein connecting all right-sided pulmonary veins toward the left atrium. Because her anatomy was suitable, the patient underwent cardiac catheterization with occlusion of the anomalous right lower pulmonary vein with an Amplatzer Vascular Plug with excellent postinterventional results.
Cite this article as: Dieks J-K, Steinmetz M, Paul T, Schneider HE. Partial Anomalous Pulmonary Venous Return into the Inferior Vena Cava in a 28-Year-Old Female: A Variant of Scimitar Syndrome Amenable to Interventional Treatment – Scimitar Syndrome Variant. Structural Heart Disease 2016;2(5):208-212. DOI: 10.12945/j.jshd.2016.013.15
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